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Headache and fainting as initial symptoms of syringomyelia associated to Arnold-Chiari and facial angiomatous nevus

B. Villamayor-Blanco, M. Arias, Á. Sesar, I. Requena-Caballero, S. Arias-Rivas, I. Pereiro-Zabala [REV NEUROL 2004;38:1035-1037] PMID: 15202081 DOI: https://doi.org/10.33588/rn.3811.2004149

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Volumen 38 | Number 11 | Nº of views of the article 16.418 | Nº of PDF downloads 1.049 | Article publication date 01/06/2004

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ABSTRACT

INTRODUCTION Syringomyelia and Arnold-Chiari malformation are two dysraphism that often appear together. Clinical manifestations are diverse although some patients remain asymptomatic for years. Syncope, supposedly due to a dysfunction of medulla baroceptors and spinal cord intermediolateral horn, is uncommon, particularly as the initial symptom.

CASE REPORT 34 year old woman, with a facial angiomatous nevus, presented with two episodes of headache followed by syncope; neurological examination was apparently normal. MRI showed mild supratentorial hydrocephalus, Arnold-Chiari malformation and cervical syringomyelia, with no vascular anomalies. CONCLUSION. This case, which shares some features with Sturge-Weber syndrome and PHACE syndrome, enhances the importance of the search for anomalies in patients with paroxistical symptoms and cutaneous lesions. KeywordsArnold-Chiari malformation Facial angiomatous Syringomyelia CategoriesCefalea y Migraña Dolor Síncope

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Nota Clínica

Headache and fainting as initial symptoms of syringomyelia associated to Arnold-Chiari and facial angiomatous nevus